Hebra A, Brown M F, McGeehin K M, Ross A J
Division of Pediatric Surgery, Children's Hospital of Philadelphia, PA 19104.
South Med J. 1993 Feb;86(2):173-6. doi: 10.1097/00007611-199302000-00005.
Cystic lesions of the mesentery, omentum, and retroperitoneum are rare; from 1956 to 1990, 22 patients had operative treatment for such lesions at our institution. They ranged in age from 1 month to 14 years; 75% were younger than 5 years. All had either an acute abdomen or, more commonly, a silent abdominal mass. In all cases, the histologic diagnosis was lymphangioma. Abdominal ultrasonography was done in all cases after 1977 except for two patients who had an acute abdomen requiring emergency exploration. A cystic abdominal mass was diagnosed in 94% of these cases, but the correct diagnosis of lymphangioma was made prior to surgery in only 24%. Mesenteric cysts are most common in the small bowel mesentery. Omental cysts usually occur singly and are easily resected, but multiple cysts predominate in the mesentery and retroperitoneum. Complete resection was accomplished in 82% of our cases. Two patients required partial bowel resection, and four had partial excision with marsupialization of the cysts. With a mean follow-up of 23 months, we have had three recurrences, but none necessitated reexploration. Extra-abdominal lesions, mainly cutaneous lymphangiomas, developed in two cases. Prognosis is good after surgical excision, but long-term follow-up is advisable because of the possibility of recurrence, even during adulthood.
肠系膜、网膜及腹膜后的囊性病变较为罕见;1956年至1990年期间,我院有22例此类病变患者接受了手术治疗。患者年龄从1个月至14岁不等;75%的患者年龄小于5岁。所有患者均有急腹症表现,或更常见的是,有腹部无症状肿块。所有病例的组织学诊断均为淋巴管瘤。1977年以后,除2例因急腹症需紧急探查的患者外,所有病例均进行了腹部超声检查。这些病例中94%被诊断为腹部囊性肿块,但术前仅24%能正确诊断为淋巴管瘤。肠系膜囊肿最常见于小肠系膜。网膜囊肿通常为单发,易于切除,但肠系膜和腹膜后的囊肿以多发为主。我们的病例中82%实现了完整切除。2例患者需要进行部分肠切除,4例进行了囊肿部分切除并开窗引流。平均随访23个月,有3例复发,但均无需再次探查。2例患者出现了腹部外病变,主要为皮肤淋巴管瘤。手术切除后预后良好,但鉴于即使在成年期也有复发的可能,建议进行长期随访。