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Exfoliative erythroderma resulting from inadequate intake of branched-chain amino acids in infants with maple syrup urine disease.

作者信息

Northrup H, Sigman E S, Hebert A A

出版信息

Arch Dermatol. 1993 Mar;129(3):384-5.

PMID:8447687
Abstract
摘要

相似文献

1
Exfoliative erythroderma resulting from inadequate intake of branched-chain amino acids in infants with maple syrup urine disease.枫糖尿症婴儿因支链氨基酸摄入不足导致的剥脱性红皮病。
Arch Dermatol. 1993 Mar;129(3):384-5.
2
Acrodermatitis enteropathica-like eruption during treatment of maple syrup urine disease: report of one case.枫糖尿症治疗期间出现的肠病性肢端皮炎样皮疹：1例报告。
Zhonghua Min Guo Xiao Er Ke Yi Xue Hui Za Zhi. 1996 Sep-Oct;37(5):357-60.
3
Nutritional deficiency dermatitis related to branched-chain amino acid restriction in a child with maple syrup urine disease.枫糖尿症患儿因支链氨基酸限制导致的营养缺乏性皮炎
Dermatol Online J. 2019 Sep 15;25(9):13030/qt53k0s8f7.
4
Nasogastric drip feeding as the only treatment of neonatal maple syrup urine disease.鼻饲滴注作为新生儿枫糖尿症的唯一治疗方法。
Pediatrics. 1993 Aug;92(2):280-3.
5
Clearance of branched chain amino acids by peritoneal dialysis in maple syrup urine disease.枫糖尿症中腹膜透析对支链氨基酸的清除作用
Adv Perit Dial. 1990;6:31-4.
6
Total branched-chain amino acids requirement in patients with maple syrup urine disease by use of indicator amino acid oxidation with L-[1-13C]phenylalanine.利用L-[1-¹³C]苯丙氨酸通过指示剂氨基酸氧化法测定枫糖尿症患者的总支链氨基酸需求量。
Am J Physiol Endocrinol Metab. 2004 Jul;287(1):E142-9. doi: 10.1152/ajpendo.00431.2003. Epub 2004 Feb 17.
7
Plasma amino acid analyses in two cases of maple syrup urine disease.两例枫糖尿症的血浆氨基酸分析
Southeast Asian J Trop Med Public Health. 1999;30 Suppl 2:138-9.
8
Branched-chain amino acid-free parenteral nutrition in the treatment of acute metabolic decompensation in patients with maple syrup urine disease.无支链氨基酸肠外营养治疗枫糖尿症患者急性代谢失代偿
N Engl J Med. 1991 Jan 17;324(3):175-9. doi: 10.1056/NEJM199101173240307.
9
[Isolated isoleucine deficiency in diet therapy of a case of maple syrup urine disease].[枫糖尿症一例饮食治疗中单纯异亮氨酸缺乏]
An Esp Pediatr. 1983 Nov;19(5):389-92.
10
[3 patients with maple syrup urine disease].
An Esp Pediatr. 1983 Nov;19(5):393-400.

引用本文的文献

1
Comprehensive Iranian guidelines for the diagnosis and management of maple syrup urine disease: an evidence- and consensus- based approach.伊朗枫糖尿症诊断与管理综合指南：基于证据和共识的方法
Orphanet J Rare Dis. 2025 Jan 7;20(1):8. doi: 10.1186/s13023-025-03533-6.
2
Skin Lesions Associated with Nutritional Management of Maple Syrup Urine Disease.与枫糖尿症营养管理相关的皮肤病变
Case Rep Dermatol Med. 2017;2017:3905658. doi: 10.1155/2017/3905658. Epub 2017 Oct 25.
3
Single amino acid supplementation in aminoacidopathies: a systematic review.
氨基酸代谢病中的单一氨基酸补充：一项系统综述。
Orphanet J Rare Dis. 2014 Jan 13;9:7. doi: 10.1186/1750-1172-9-7.