Allen S W, Whitfield J M, Clarke D R, Sujansky E, Wiggins J W
Department of Pediatrics, University of Colorado Health Science Center, Denver.
Pediatr Cardiol. 1993 Jan;14(1):58-61. doi: 10.1007/BF00794850.
Pulmonary arteriovenous malformation (PAVM) is a rare cause of cyanosis in the newborn with nine previously reported cases. Typical signs at presentation include cyanosis, murmur, and congestive heart failure. Abnormality on chest x-ray is common with cardiomegaly, oligemia, and focal pulmonary density. There is a male predominance, unlike older children and adults with PAVM. Familial cases of PAVM have been reported with Osler-Weber-Rendu syndrome. We report a familial case of PAVM presenting in the newborn.
肺动静脉畸形(PAVM)是新生儿发绀的罕见原因,此前已有9例报道。典型的临床表现包括发绀、杂音和充血性心力衰竭。胸部X线异常常见,表现为心脏扩大、肺血减少和局灶性肺部密度增高。与年长儿童和成人的PAVM不同,新生儿PAVM以男性居多。有报道称PAVM的家族性病例与遗传性出血性毛细血管扩张症相关。我们报告了1例新生儿家族性PAVM病例。