The management of portal hypertension in cystic fibrosis.

Schuster S R, Shwachman H, Toyama W M, Rubino A, Taik-Khaw K

J Pediatr Surg. 1977 Apr;12(2):201-6. doi: 10.1016/s0022-3468(77)80008-0.

We have found that with proper selection and preoperative preparation, a major portosystemic shunt can be done with considerable safety in a majority of cystic fibrosis patients and thus provide them with significant palliation and improved quality of life.