Smith N M, Byard R W, Vigneswaran R, Bourne A J, Knight B
Department of Histopathology, Adelaide Children's Hospital, North Adelaide, South Australia.
Pediatr Cardiol. 1993 Mar;14(2):82-5. doi: 10.1007/BF00796984.
A female infant with multiple congenital abnormalities and a right atrial "mass" on echocardiography is reported. Her general condition at birth was poor, and the chest x-ray showed cardiomegaly. Echocardiography demonstrated the usual atrial arrangement and concordant atrioventricular and ventriculoarterial connections with a mobile right atrial mass. Death occurred at 3 days of age and subsequent postmortem examination revealed a hollow, tube-like sinus venosus remnant mobile between right atrium and ventricle with numerous other abnormalities of the heart, including left heart hypoplasia and tubular hypoplasia of the aortic arch. Filling of the sinus venosus remnant with blood had resulted in an echocardiographic appearance suggestive of a right atrial tumor.
报告了一名患有多种先天性异常且超声心动图显示右心房有“肿块”的女婴。她出生时一般状况较差,胸部X线显示心脏扩大。超声心动图显示心房排列正常,房室和心室动脉连接一致,伴有一个可移动的右心房肿块。患儿于3日龄时死亡,随后的尸检发现一个中空的管状静脉窦残余物在右心房和心室之间移动,同时还存在许多其他心脏异常,包括左心发育不全和主动脉弓管状发育不全。静脉窦残余物充血导致超声心动图表现提示右心房肿瘤。