Cacoub P, Benhamou Y, Barbet P, Piette J C, Le Cae A, Chaussade S, Cadranel J F, Callard P, Opolon P, Godeau P
Department of Internal Medicine, Hopital La Pitié-Salpétière, Paris, France.
J Rheumatol. 1993 Feb;20(2):377-81.
We describe the first case of a patient with systemic lupus erythematosus in which clinical and radiological features, small bowel manometry and histological studies were consistent with the diagnosis of chronic intestinal pseudoobstruction. Our patient developed a fatal form of lupus with cerebral angiitis and tubulointerstitial lupus nephritis, with no sign of progressive systemic sclerosis or dermatopolymyositis. Postmortem examination confirmed the presence of an extensive fibrotic process in the muscularis layers, whereas the muscularis mucosae and the innervation of the digestive wall were spared.
我们描述了首例系统性红斑狼疮患者,其临床和放射学特征、小肠测压及组织学研究结果均符合慢性假性肠梗阻的诊断。我们的患者发展为伴有脑血管炎和肾小管间质性狼疮肾炎的致死性狼疮,无进行性系统性硬化症或皮肌炎迹象。尸检证实肌层存在广泛纤维化过程,而黏膜肌层和消化道壁神经支配未受影响。