Treiger B F, Khazan R, Goldman S M, Marshall F F
Department of Urology, James Buchanan Brady Urological Institute, Johns Hopkins Medical Institutions, Baltimore, Maryland.
Urology. 1993 May;41(5):455-7. doi: 10.1016/0090-4295(93)90507-7.
A case of renal cell carcinoma in a patient with situs inversus totalis is reported. Only 8 cases of malignant neoplasms have been reported in situs inversus totalis, and our case represents the second case report of renal cell carcinoma in a patient with situs inversus totalis. The frequency of situs inversus totalis is between 1 in 8,000 and 1 in 20,000. Cardiac and pulmonary anomalies are common in patients with situs inversus totalis. Renal anomalies, including agenesis, dysplasia, hypoplasia, ectopia, polycystic kidney, and horseshoe kidney, have been reported. Because of the association between situs inversus and cardiac, pulmonary, renal, and vascular anomalies, management of the patient with situs inversus and urologic disease requires careful preoperative evaluation.
报告了一例全内脏转位患者发生肾细胞癌的病例。全内脏转位患者仅报告过8例恶性肿瘤，我们的病例是全内脏转位患者发生肾细胞癌的第二例报告。全内脏转位的发生率在8000分之一至20000分之一之间。心脏和肺部异常在全内脏转位患者中很常见。已报告有肾脏异常，包括肾缺如、发育异常、发育不全、异位、多囊肾和马蹄肾。由于内脏转位与心脏、肺部、肾脏和血管异常之间存在关联，对患有内脏转位和泌尿系统疾病的患者进行治疗需要仔细的术前评估。
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