Gatto E M, Fernández Pardal M M, Micheli F, González M A, Daru V D
Instituto de Neurocirugía y Neurología, Sanatorio Mitre.
Rev Clin Esp. 1993 May;192(8):380-2.
Prolongation of the QT interval, either on a congenital or an acquired basis, is associated with an increased likelihood of malignant ventricular arrhythmias with a high rate of morbimortality. Symptoms are variables, and patients may develop seizures, syncope and sudden death. Herein we report a young woman 17 years old with long QT syndrome, seizures and recurrent attacks of syncope; her initial diagnosis was primary epilepsy. An electrocardiogram performed 3 years after the initials symptoms was able to make the diagnosis long QT syndrome. The specific treatment controlled the malignant ventricular arrhythmias and the symptomatic status of this patient.
QT间期延长,无论是先天性还是后天性的,都与恶性室性心律失常的可能性增加相关,且病死亡率很高。症状多样,患者可能会出现癫痫发作、晕厥和猝死。在此,我们报告一名17岁的年轻女性,患有长QT综合征、癫痫发作和反复发作的晕厥;她最初被诊断为原发性癫痫。初始症状出现3年后进行的心电图检查得以诊断出长QT综合征。针对性治疗控制了该患者的恶性室性心律失常和症状状态。