Pfau A, Landthaler M
Department of Dermatology, University of Regensburg, Germany.
Dermatology. 1995;191(2):161-3. doi: 10.1159/000246538.
A young girl has undergone the typical skin manifestations of incontinentia pigmenti, leaving now only discrete hyperpigmentation on the flexor sides of the lower extremities. Each time when she has a feverish infection, a recurrence of inflammation can be seen within the hyperpigmented areas. At the same time when the fever subsides, the acute skin manifestations disappear as well. The combination of recurrent inflammatory skin manifestations within the hyperpigmented skin areas of incontinentia pigmenti and fever is unique. The reasons for this phenomenon and for its strict limitation to the areas of incontinentia pigmenti remain unclear.
一名年轻女孩曾出现色素失禁症的典型皮肤表现，如今仅在下肢屈侧留有散在的色素沉着。每次她发生发热性感染时，色素沉着区域内都会再次出现炎症。同时，当发热消退时，急性皮肤表现也会消失。色素失禁症色素沉着皮肤区域内反复出现的炎症性皮肤表现与发热同时出现，这一情况很独特。这种现象的原因以及为何严格局限于色素失禁症区域尚不清楚。
