Matthias C, Terstegge K, Siemes H
Department of Otorhinolaryngology, Virchow Hospital of Humboldt University, Berlin, Germany.
Ann Otol Rhinol Laryngol. 1995 Nov;104(11):853-7. doi: 10.1177/000348949510401105.
Progressive facial hemiatrophy (PFH) is characterized by slowly progressive atrophy of subcutaneous tissue. Bone, muscles, nerves, the eye, and the brain may be affected by atrophy. Four patients suffering from various otorhinolaryngological complications of PFH or Romberg's disease are reported. Unilateral hearing loss could be located in the inner ear of one patient by audiologic examination. Localized bone destruction and disintegration of a portion of the anterior wall of the frontal sinus were observed in a patient after more than three decades. Marked shrinking of the homolateral parotid gland and homolateral masticatory spasm are reported as further otorhinolaryngological manifestations. The various complications of PFH call for close interdisciplinary cooperation.
进行性面部半侧萎缩症（PFH）的特征是皮下组织进行性缓慢萎缩。骨骼、肌肉、神经、眼睛和大脑可能会受到萎缩影响。本文报告了4例患有PFH或Romberg病各种耳鼻咽喉科并发症的患者。通过听力检查，一名患者的单侧听力损失定位于内耳。一名患者在三十多年后观察到额窦前壁部分的局部骨质破坏和崩解。同侧腮腺明显萎缩和同侧咀嚼肌痉挛被报告为进一步的耳鼻咽喉科表现。PFH的各种并发症需要密切的多学科合作。
