[Familial sacrococcygeal teratoma].

Familial sacrococcygeal teratomas are very rare. Up to now, only 8 kindreds (31 patients, including 1 Japanese kindreds) have been reported. All cases are Altman type IV variety. The tumor complex consists of a presacral teratoma and sacrococcygeal bony anomalies. The most common symptoms are constipation and anorectal stenosis. Two patients died. One died of meningitis following removal of a large benign tumor because of communication with a spinal arachinoid space. The other, with a large benign tumor, died as a result of malignant change, 10 years later after the first operation. The incidence of malignant change of familiar sacrococcygeal teratoma is rare in comparison with that of non-familiar sacrococcygeal teratomas.