Dickinson J E, Marshall L R, Phillips J M, Barr A L
King Edward Memorial Hospital for Women, Perth, Western Australia.
Am J Perinatol. 1995 Sep;12(5):333-5. doi: 10.1055/s-2007-994489.
Fetomaternal alloimmune thrombocytopenia (FMAT) arises from maternal-fetal platelet antigen incompatibility, which stimulates the production of maternal immunoglobulin G (IgG) platelet-specific antibody. Transplacental passage of this antibody results in fetal platelet destruction and consequent thrombocytopenia. Sequelae of thrombocytopenia may be observed in both the fetus and neonate with intracranial hemorrhage occurring in approximately 10 to 30% of affected infants. No antenatal universal screening test is currently available to detect the 50% of cases occurring in the first pregnancy. The recurrence rate in subsequent pregnancies is 75 to 85%, with a tendency to increasing disease severity. Paternal platelet genotyping is recommended to assist in risk counseling following an affected pregnancy. Prenatal therapeutic strategies are aimed at elevating the fetal platelet count in affected pregnancies and thus decreasing hemorrhagic sequelae. The most effective treatment regimen is uncertain, but encouraging results are reported with the use of maternal intravenous gamma globulin. We report our experience in the antenatal diagnosis and management of FMAT.
胎儿母体型同种免疫性血小板减少症(FMAT)源于母胎血小板抗原不相容,这会刺激母体产生免疫球蛋白G(IgG)血小板特异性抗体。该抗体经胎盘传递导致胎儿血小板破坏及随之而来的血小板减少。血小板减少的后遗症在胎儿和新生儿中均可能出现,约10%至30%的患病婴儿会发生颅内出血。目前尚无产前通用筛查试验可检测出首次妊娠中发生的50%的病例。后续妊娠的复发率为75%至85%,且疾病严重程度有增加趋势。建议进行父亲血小板基因分型,以在有患病妊娠史后协助进行风险咨询。产前治疗策略旨在提高患病妊娠中的胎儿血小板计数,从而减少出血后遗症。最有效的治疗方案尚不确定,但使用母体静脉注射丙种球蛋白报告了令人鼓舞的结果。我们报告了我们在FMAT产前诊断和管理方面的经验。