Brown J, Ashworth A, Gydesen S, Sorensen A, Rossor M, Hardy J, Collinge J
Department of Biochemistry and Molecular Genetics, St Mary's Hospital Medical School, London, UK.
Hum Mol Genet. 1995 Sep;4(9):1625-8. doi: 10.1093/hmg/4.9.1625.
A significant minority of degenerative dementias lack distinctive inclusion bodies, plagues or tangles on pathological examination. Half of these cases have a positive family history of dementia. We have studied the largest published family with such a dementia and mapped the disease locus to a 12 cM region of chromosome 3 spanning the centromere. Haplotype analysis demonstrates a common region shared between all affected individuals between the markers D3S1284 and D3S1603. Like a number of other late onset neurodegenerative diseases, the disease presents at an earlier age when paternally inherited.