Bonavita V, Messina C, Savettieri G
Riv Patol Nerv Ment. 1977 Feb;97(1):18-25.
An atypical case of "Foix-Chavany syndrome", is described. A definite diagnosis could be achieved through an electromyographic and reflessological investigation (jaw reflex, blink reflex, perioral reflex), when a poor clinical history was not helping towards a definite diagnostic conclusion. It is proposed that the diagnosis of "Foix-Chavany syndrome" should not be limited only to classical "facial diplegia of cortical origin" or to "facio-linguo-pharyngo-laryngo-masseter paralysis of cortico-subcortical origin". Considering the great clinical variability of a syndrome with a common anatomical substrate, it is proposed to use the eponym for all syndromes characterized by: 1) a motor deficit in the cephalic district with relative integrity of motor function of the limbs; 2) a dissociation between loss of voluntary motility and preservation of reflex and automatic motility.
本文描述了一例“福瓦-沙瓦尼综合征”的非典型病例。当临床病史不明确无法得出明确诊断结论时,可通过肌电图和反射学检查(下颌反射、瞬目反射、口周反射)来明确诊断。本文提出,“福瓦-沙瓦尼综合征”的诊断不应仅局限于经典的“皮质源性面瘫”或“皮质-皮质下源性面-舌-咽-喉-咬肌麻痹”。鉴于具有共同解剖学基础的该综合征临床变异性很大,本文建议对所有具有以下特征的综合征使用该名称:1)头部区域运动功能缺损,肢体运动功能相对完整;2)随意运动丧失与反射和自动运动保留之间的分离。