Razack N, Page L K
Department of Neurological Surgery, University of Miami School of Medicine, Florida, USA.
Neurosurgery. 1995 Nov;37(5):1006-8. doi: 10.1227/00006123-199511000-00023.
Split notochord syndrome includes a cleft of the vertebral column associated with malformation of the central nervous system. Fourteen cases involving the lumbosacral spine have been reported in the literature. We report on a female neonate who had intact function of her lower extremities, a posterior midline lumbar defect bounded by two complete spinal canals that contained two spinal cords. A meningocele, a large bowel fistula, and a mature teratoma protruded through the cleft. The baby is doing well after repair of the anomaly and placement of a ventriculoperitoneal shunt.
分裂脊索综合征包括与中枢神经系统畸形相关的脊柱裂。文献中已报道了14例累及腰骶椎的病例。我们报告了一名女性新生儿，其下肢功能完好，腰椎后正中线有一缺损，由两个完整的椎管界定，椎管内有两条脊髓。一个脑脊膜膨出、一个大肠瘘和一个成熟畸胎瘤从裂隙中突出。在修复该畸形并置入脑室腹腔分流管后，婴儿情况良好。
