[Porokeratosis plantaris, palmaris et disseminataa with multiple filiform hyperkeratoses and nail dystrophy].

We report on a family with porokeratosis plantaris, palmaris et disseminata with a very unusual clinical manifestation. The father showed an association of multiple filiform hyperkeratosis on the trunk with sparing of the palms and soles. In addition, this patient featured secondary nail dystrophy owing to porokeratosis. The daughter had an unusual course: the disease started on the trunk and did not spread to the palms and soles until later. In general the reverse is true.