Tron A M, Piperno M, Bouvier R, Conrozier T, Vignon E
Service de rhumatologie, hôpital Edouard-Herriot, Lyon, France.
Rev Med Interne. 1995;16(11):850-3. doi: 10.1016/0248-8663(96)80801-0.
Primary systemic amyloidosis rarely affects the walls of small and medium-sized vessels. We report a case of primary AL amyloidosis masquerading as giant cell arteritis at the onset of the disease, revealed by the temporal arteritis biopsy, and successfully treated by corticotherapy for three years. Histology of temporal arteritis confirms the diagnosis of amyloidosis (characteristic birefringence with Congo red). We discuss in this case the diagnosis of primary amyloidosis revealed by Horton disease, or the coincidental association of these two diseases.
原发性系统性淀粉样变性很少累及中小血管壁。我们报告一例原发性AL淀粉样变性病例，该病例在疾病初期伪装为巨细胞动脉炎，经颞动脉活检确诊，并通过皮质激素治疗成功治愈三年。颞动脉炎的组织学检查证实了淀粉样变性的诊断（刚果红染色呈现特征性双折射）。在本病例中，我们讨论了由霍顿病揭示的原发性淀粉样变性的诊断，或这两种疾病的巧合关联。
