Nishimura T, Mori K, Sada Y, Fujii M
Department of Neurosurgery, Taiju-kai Foundation (Medical Corporation) General Hospital, Kagawa, Japan.
Neurol Med Chir (Tokyo). 1995 Dec;35(12):876-81. doi: 10.2176/nmc.35.876.
A female neonate with myelomeningocele but without Chiari type II malformation suffered from apneic spells. Magnetic resonance imaging showed no obvious brainstem anomaly. Brainstem auditory evoked potentials were initially abnormal and subsequently deteriorated during the 6 months after birth. The brainstem deficits were not reversed by a ventriculoperitoneal shunt. She died of respiratory distress and cardiac failure at 2 years of age. This case indicates an intrinsic dysfunction in the brainstem of patients with myelomeningocele not complicated by Chiari type II malformation.
一名患有脊髓脊膜膨出但无Chiari II型畸形的女新生儿出现呼吸暂停发作。磁共振成像显示脑干无明显异常。脑干听觉诱发电位最初异常，且在出生后的6个月内逐渐恶化。脑室腹腔分流术未能逆转脑干功能缺损。她在2岁时死于呼吸窘迫和心力衰竭。该病例表明，未合并Chiari II型畸形的脊髓脊膜膨出患者存在脑干内在功能障碍。
