Van Laere J E
Rev Neurol (Paris). 1977 Feb;133(2):119-24.
The author reports a new case of chronic progressive bulbo-pontine paralysis with deafness. This case differed from other cases previously published on the basis of the later age of onset of labio-glosso-laryn-geal paralysis, by the absence of any vestibular changes despite bilateral involvement of the acoustic centres and above all by the normality of deep tendon reflexes. The author feels that chronic progressive vulvo-pontine paralysis with deafness is a specific individual condition, worthy of consideration as an autonomic clinical entity.
作者报告了一例伴有耳聋的慢性进行性延髓脑桥麻痹新病例。该病例与先前发表的其他病例不同,表现为唇舌喉麻痹发病年龄较晚,尽管听觉中枢双侧受累但无前庭变化,最重要的是深腱反射正常。作者认为伴有耳聋的慢性进行性延髓脑桥麻痹是一种特殊的个体病症,值得作为一种独立的临床实体加以考虑。