Fourcade L, Vahdat B, Panagides D, Yvorra S, Bonnet J L, Bory M
Service de cardiologie A, CHU Timone, Marseille.
Arch Mal Coeur Vaiss. 1996 Jan;89(1):103-6.
The authors report the case of a pulmonary arteriovenous fistula presenting with dyspnoea and cyanosis in a young adult. The malformation was situated on the proximal pulmonary vessels and was cured by surgical correction. The diagnostic value of the clinical signs and complementary investigations of this rare conditions, often detected during adulthood, is discussed. The functional tolerance of the condition is often variable. Oxygen desaturation of arterial blood indicates a right-to-left shunt. Pulmonary angiography enables visualisation of the lesions and guides surgical management. The prevalence of complications of this condition is not well known, but the potential severity is an argument for therapeutic intervention. Embolisation techniques are developing but there is a risk of a systemic embolism. Surgery is the reference for the treatment of proximal fistulae, its curative effect being immediate and definitive.
作者报告了一例年轻成年人因肺动静脉瘘出现呼吸困难和发绀的病例。该畸形位于近端肺血管，通过手术矫正得以治愈。文中讨论了这种成年期常被发现的罕见病症的临床体征及辅助检查的诊断价值。该病症的功能耐受性通常因人而异。动脉血氧饱和度降低表明存在右向左分流。肺血管造影可显示病变并指导手术治疗。这种病症并发症的发生率尚不清楚，但潜在的严重性是进行治疗干预的依据。栓塞技术不断发展，但存在全身栓塞的风险。手术是近端瘘管治疗的首选方法，其疗效立竿见影且确切。
