Miura H, Kashiwamura H, Oyama Y, Murakami K, Itoh J
Department of Neurology, Hachinohe City Hospital, Japan.
No To Shinkei. 1996 Jan;48(1):77-80.
A 47-year-old woman had an episode of severe headache for a few days. She suddenly experienced right leg weakness and sensory loss. A CT scan revealed subcortical hematoma at the left parietal lobe on admission. Cerebral angiography showed multiple vascular irregularities such as segmentally narrow or sausage-like dialatated areas. Her laboratory studies were entirely normal including antinuclear antibody and coagulation tests. The diagnosis of isolated angiitis of the CNS was made and she responded well to the low dose corticosteroid therapy. Repeated cerebral angiography two months after the onset demonstrated most of the areas of segmental irregularity had improved with a few unchanged areas. Some cerebral angiitis do exist that respond well to corticosteroid therapy, therefore, early diagnosis and treatment are suggested in cases of angiitis.
一名47岁女性出现严重头痛症状数天。她突然出现右腿无力和感觉丧失。入院时CT扫描显示左顶叶皮质下血肿。脑血管造影显示多处血管不规则，如节段性狭窄或腊肠样扩张区域。她的实验室检查完全正常，包括抗核抗体和凝血试验。诊断为中枢神经系统孤立性血管炎，她对低剂量皮质类固醇治疗反应良好。发病两个月后重复脑血管造影显示，大多数节段性不规则区域有所改善，少数区域未改变。确实存在一些对皮质类固醇治疗反应良好的脑血管炎，因此，对于血管炎病例建议早期诊断和治疗。
