Gotts E E, Liemohn W P
Biol Psychiatry. 1977 Jun;12(3):413-23.
Behavioral characteristics of three children with Broad Thumb-Hallux or Rubinstein-Taybi (R-T) syndrome were compared with those of a somewhat comparable clinic sample (N - 15) of children with organic syndromes and retardation. A number of mutual, behavioral resemblances of the three R-T children to each other were found to be absent or less prominent in the comparison group; these included: (i) the R-T children were more emotional and excitable; (ii) more often had nightmares and engaged in self-stimulation; (iii) had greater difficulty getting over anger (pouted); (iv) were friendly and more readily accepted social contacts; (v) had short attention span; and (vi) experienced more difficulty in planning motor acts, and in executing locomotor and oculomotor skills. The pattern of R-T mutual resemblances and their differences from other clinic children logically suggest what may be the behavioral characteristics of children with the R-T syndrome. Educational and child-management suggestions are provided based on the observed and tested characteristics which are presumably related to the R-T syndrome.
将三名患有宽拇指-拇趾或鲁宾斯坦-泰比（R-T）综合征的儿童的行为特征与一组患有器质性综合征和智力发育迟缓的儿童（N = 15）的行为特征进行了比较，后者在临床上与之有一定可比性。研究发现，三名R-T儿童之间的一些共同行为特征在对照组中并不存在或不那么明显；这些特征包括：（i）R-T儿童情绪更激动、更易兴奋；（ii）更经常做噩梦并进行自我刺激；（iii）更难消除愤怒情绪（撅嘴）；（iv）友善且更容易接受社交接触；（v）注意力持续时间短；（vi）在计划运动行为以及执行运动和眼球运动技能方面遇到更多困难。R-T儿童之间的共同特征模式以及他们与其他临床儿童的差异从逻辑上表明了R-T综合征儿童可能具有的行为特征。基于观察和测试的、可能与R-T综合征相关的特征，提供了教育和儿童管理方面的建议。
