Kaipiainen-Seppänen O, Jantunen E, Kuusisto J, Marin S
Department of Medicine, Kuopio University Hospital, Finland.
J Rheumatol. 1996 Apr;23(4):779-81.
A middle aged man showed retroperitoneal fibrosis with signs of vasculitis verified by biopsy of the retroperitoneal mass. Antineutrophil cytoplasmic antibodies (ANCA) with cytoplasmic staining pattern (cANCA) were strongly positive, although there were no clinical or histological signs of Wegener's granulomatosis. No cases of cANCA associated retroperitoneal fibrosis have been described except in connection with Wegener's granulomatosis. ANCA have been found to associate with any inflammatory disorders. This observation may broaden the clinical spectrum of cANCA positive vasculitides.
一名中年男性表现为腹膜后纤维化，伴有血管炎体征，经腹膜后肿块活检证实。尽管没有韦格纳肉芽肿的临床或组织学体征，但胞浆型抗中性粒细胞胞浆抗体（cANCA）呈强阳性。除了与韦格纳肉芽肿相关外，尚未有cANCA相关性腹膜后纤维化的病例报道。已发现ANCA与任何炎症性疾病有关。这一观察结果可能会拓宽cANCA阳性血管炎的临床谱。
