Cystic fibrosis therapy--where we are and how we got there.
作者信息
Gruenert D C
出版信息
West J Med. 1996 Apr;164(4):361-2.
Abstract
摘要
相似文献
1
Cystic fibrosis therapy--where we are and how we got there.囊性纤维化治疗——我们所处的位置以及我们如何走到这一步。
West J Med. 1996 Apr;164(4):361-2.
2
Topical cystic fibrosis transmembrane conductance regulator gene replacement for cystic fibrosis-related lung disease.用于囊性纤维化相关肺部疾病的局部囊性纤维化跨膜传导调节因子基因替代疗法。
Paediatr Respir Rev. 2017 Mar;22:47-49. doi: 10.1016/j.prrv.2016.10.005. Epub 2016 Nov 5.
3
Current progress in cystic fibrosis: is this a disease elusive to therapy?
Pulm Pharmacol Ther. 2008 Aug;21(4):585-7. doi: 10.1016/j.pupt.2008.01.002. Epub 2008 Jan 26.
4
[Protein repair therapy in cystic fibrosis].[囊性纤维化的蛋白质修复疗法]
Rev Prat. 2003 Jan 15;53(2):163-6.
5
Evaluation of repeat administration of a replication deficient, recombinant adenovirus containing the normal cystic fibrosis transmembrane conductance regulator cDNA to the airways of individuals with cystic fibrosis.对携带正常囊性纤维化跨膜传导调节因子cDNA的复制缺陷型重组腺病毒重复给药至囊性纤维化患者气道的评估。
Hum Gene Ther. 1995 May;6(5):667-703. doi: 10.1089/hum.1995.6.5-667.
6
Status of gene therapy for cystic fibrosis lung disease.囊性纤维化肺病的基因治疗现状。
J Clin Invest. 1999 Feb;103(4):441-5. doi: 10.1172/JCI6330.
7
[New therapeutic approaches in cystic fibrosis].[囊性纤维化的新治疗方法]
Pharm Unserer Zeit. 2008;37(5):354-5. doi: 10.1002/pauz.200890069.
8
Gene therapy for cystic fibrosis.囊性纤维化的基因治疗。
J Gene Med. 2001 Sep-Oct;3(5):409-17. doi: 10.1002/jgm.200.
9
[Gene therapy of cystic fibrosis].[囊性纤维化的基因治疗]
Schweiz Med Wochenschr. 1999 Nov 20;129(46):1779-83.
10
Cystic fibrosis gene therapy: the first trial.囊性纤维化基因治疗：首例试验。
Arch Dis Child. 2015 Sep;100(9):844. doi: 10.1136/archdischild-2015-309332. Epub 2015 Jul 23.
本文引用的文献
1
2
Cystic fibrosis in adults. From researcher to practitioner.成人囊性纤维化。从研究者到从业者。
West J Med. 1996 Apr;164(4):321-34.
3
Inflammatory cytokines in cystic fibrosis lungs.囊性纤维化肺部中的炎性细胞因子。
Am J Respir Crit Care Med. 1995 Dec;152(6 Pt 1):2111-8. doi: 10.1164/ajrccm.152.6.8520783.
4
Cellular and humoral immune responses to viral antigens create barriers to lung-directed gene therapy with recombinant adenoviruses.针对病毒抗原的细胞免疫和体液免疫反应对重组腺病毒介导的肺靶向基因治疗形成了障碍。
J Virol. 1995 Apr;69(4):2004-15. doi: 10.1128/JVI.69.4.2004-2015.1995.
5
Cross-sectional and longitudinal studies of naturally occurring antibodies to Pseudomonas aeruginosa in cystic fibrosis indicate absence of antibody-mediated protection and decline in opsonic quality after infection.对囊性纤维化患者体内抗铜绿假单胞菌天然抗体的横断面研究和纵向研究表明，抗体介导的保护作用不存在，且感染后调理素质量下降。
J Infect Dis. 1995 Aug;172(2):453-61. doi: 10.1093/infdis/172.2.453.
6
A cystic fibrosis mutation associated with mild lung disease.一种与轻度肺部疾病相关的囊性纤维化突变。
N Engl J Med. 1995 Jul 13;333(2):95-9. doi: 10.1056/NEJM199507133330204.
7
Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis.囊性纤维化患者呼吸上皮细胞跨膜生物电位差增加。
N Engl J Med. 1981 Dec 17;305(25):1489-95. doi: 10.1056/NEJM198112173052502.
8
Chloride impermeability in cystic fibrosis.囊性纤维化中的氯离子不渗透性
Nature. 1983 Feb 3;301(5899):421-2. doi: 10.1038/301421a0.
9
Abnormal ion permeation through cystic fibrosis respiratory epithelium.异常离子透过囊性纤维化呼吸道上皮。
Science. 1983 Sep 9;221(4615):1067-70. doi: 10.1126/science.6308769.
10
Cystic fibrosis decreases the apical membrane chloride permeability of monolayers cultured from cells of tracheal epithelium.囊性纤维化降低了从气管上皮细胞培养的单层细胞顶端膜的氯离子通透性。
Proc Natl Acad Sci U S A. 1985 Sep;82(18):6167-71. doi: 10.1073/pnas.82.18.6167.
Zotero 插件