Rubin M, Mackenzie C R
Department of Neurology, Hospital for Special Surgery, New York, NY, USA.
Electromyogr Clin Neurophysiol. 1996 Apr-May;36(3):145-9.
A 35-year-old woman presented with a 4 year history of stepwise sensory loss which progressed in an asymmetrical fashion (mononeuropathy multiplex) and developed into a relatively symmetric polyneuropathy which was purely sensory by clinical and electrodiagnostic criteria. Sural nerve biopsy revealed demyelination with axonal sparing. Extensive laboratory evaluation failed to reveal a definite cause. This case is unique among well-documented cases of chronic inflammatory demyelinating polyneuropathy (CIDP) in that it is purely sensory by both clinical and electrodiagnostic criteria, and may represent a distinct entity rather than an extension of the spectrum of CIDP.
一名35岁女性，有4年逐步进展的感觉丧失病史，呈不对称性进展（多灶性单神经病），并发展为相对对称的多发性神经病，根据临床和电诊断标准，该多发性神经病为纯感觉性。腓肠神经活检显示脱髓鞘且轴突保留。广泛的实验室检查未能发现明确病因。在已充分记录的慢性炎症性脱髓鞘性多发性神经病（CIDP）病例中，该病例具有独特性，因为根据临床和电诊断标准，它均为纯感觉性，可能代表一种独特的疾病实体，而非CIDP谱系的延伸。
