Pul N, Pul M
Cocuk Sağliği ve Hastaliklari Uzmani, Edirne, Turkey.
Eur J Pediatr. 1996 Jan;155(1):18-9. doi: 10.1007/BF02115620.
The Rapunzel syndrome (RS), is a rare form of gastric trichobezoar extending throughout the bowel. We report on a patient with RS causing gastric perforation and discuss the aetiology, pathogenesis, diagnosis and treatment of this unusual syndrome. RS is found characteristically in girls with varying gastro-intestinal symptoms. The recommended treatment for large or complicated trichobezoars is surgery. Psychiatric follow up is essential to diminish the frequency of recurrence.
Symptoms of trichobezoars are nonspecific and may mimic those of other pathological gastro-intestinal conditions. Early diagnosis and treatment of this condition is of prime importance and may avoid later fatal complications.
长发公主综合征(RS)是一种罕见的胃内毛石症,可延伸至整个肠道。我们报告一例因RS导致胃穿孔的患者,并讨论这种罕见综合征的病因、发病机制、诊断和治疗。RS典型地见于有各种胃肠道症状的女孩。对于大的或复杂的毛石症,推荐的治疗方法是手术。进行精神科随访对于减少复发频率至关重要。
毛石症的症状不具特异性,可能与其他病理性胃肠道疾病的症状相似。对这种疾病进行早期诊断和治疗至关重要,可避免后期出现致命并发症。