先天性双侧颧骨-下颌骨融合伴下颌发育不全。

Congenital bilateral zygomatico-mandibular fusion with mandibular hypoplasia.

作者信息

Kamata S, Satoh K, Uemura T, Onizuka T

机构信息

Department of Plastic and Reconstructive Surgery, Showa University School of Medicine, Tokyo, Japan.

出版信息

Br J Plast Surg. 1996 Jun;49(4):251-3. doi: 10.1016/s0007-1226(96)90062-4.

DOI:10.1016/s0007-1226(96)90062-4

PMID:8757678

Abstract

We report a very rare case of congenital bilateral zygomatico-mandibular fusion with mandibular hypoplasia. Soon after birth, the patient underwent tracheotomy because of upper airway obstruction. At the age of one and a half years, reconstruction of the temporomandibular joint and lengthening of the ramus with a costochondral graft were performed. Only a few cases of congenital bony syngnathia revealed in this case have been described in the literature.

摘要

我们报告一例极为罕见的先天性双侧颧骨-下颌骨融合伴下颌发育不全病例。患儿出生后不久，因上呼吸道梗阻接受了气管切开术。一岁半时，进行了颞下颌关节重建及肋软骨移植下颌支延长术。文献中仅描述了少数几例如此病例所呈现的先天性骨性颌骨融合。