Kamoun A, Hammou A, Chaouachi S, Bellagha I, Lakhoua R
Service de Pédiatrie, Hôpital Charles Nicolle, Tunis, Tunisie.
Ann Radiol (Paris). 1995;38(7-8):440-6.
The authors report the radiological signs observed in 14 patients between the ages of 3 months and 16 years, suffering from type I primary hyperoxaluria. Four of these patients were being treated conservatively for renal failure and ten had reached end-stage renal failure. Stones were demonstrated in 9 patients. Nephrocalcinosis was present on the plain abdominal x-ray in 6 patients before dialysis, and in all patients dialysed for more than 3 months. Bone signs characteristic of type I primary hyperoxaluria were only observed in children with end-stage renal failure. Metaphyseal dense bands were revealed in 5 patients. Metaphyseal clear bands, observed in 4 patients, occurred later and appeared to replace dense bands which moved towards the diaphysis. The other signs detected were osteosclerosis of the vertebrae and ilium (4 patients) and epiphyseal subchondral clear bands (one patient).
作者报告了14例年龄在3个月至16岁之间的I型原发性高草酸尿症患者的放射学表现。其中4例患者因肾衰竭接受保守治疗，10例已发展至终末期肾衰竭。9例患者发现有结石。6例患者在透析前的腹部平片上显示有肾钙质沉着，而所有透析超过3个月的患者均有此表现。I型原发性高草酸尿症的典型骨表现仅在终末期肾衰竭患儿中观察到。5例患者出现干骺端致密带。4例患者出现干骺端透亮带，出现时间较晚，似乎替代了向骨干移动的致密带。其他检测到的表现包括椎体和髂骨骨质硬化（4例患者）以及骨骺软骨下透亮带（1例患者）。
