[Persistent acral papulous mucinosis].

INTRODUCTION

Acral persistent papular mucinosis is an uncommon skin disease with characteristic mucin deposits in the medial layer of the derma. In the Rongioletti and Rebora classification, this disease belongs to the group of specific cutaneous mucinoses.

CASE REPORT

A 14-year-old girl consulted for symmetrical papular lesions on the back of the hand and wrists. The first manifestations had occurred at the age of 3 years. Laboratory tests were positive for antinuclear antibodies at 1/320. The histology and the clinical presentation led to the diagnosis of acral persistent papular mucinosis.

DISCUSSION

This case shows that manifestations of acral persistent papular mucinosis can occur early in childhood. This disease may be a single clinical entity or an attenuated clinical expression of papular mucinosis. Clinical and laboratory observation were required for our patient.