Gillard P, Bataille B, Chauvet-Jauseau M F, Noyelle J M, Vige F, Bréheret J
Service de Gynécologie-Obstétrique, Centre Hospitalier, Niort.
J Gynecol Obstet Biol Reprod (Paris). 1996;25(3):294-6.
A 24-year-old woman with Rendu-Osler-Weber disease presented an intracranial hematoma during pregnancy. The main localizations of the Rendu-Osler-Weber disease, an inborn disease, are discussed. Neurological complications are rare. Vascular malformations are more fragile during pregnancy. The obstetrical attitude depends on the organ involved and the severity of the complications.
一名患有遗传性出血性毛细血管扩张症的24岁女性在孕期出现颅内血肿。本文讨论了这种先天性疾病——遗传性出血性毛细血管扩张症的主要病变部位。神经系统并发症较为罕见。血管畸形在孕期更为脆弱。产科处理方式取决于受累器官及并发症的严重程度。