Neau J P, Boissonnot L, Boutaud P, Fontanel J P, Gil R, Lefèvre J P
Rev Med Interne. 1987 Jan-Feb;8(1):75-8. doi: 10.1016/s0248-8663(87)80111-x.
Rendu-Osler-Weber disease is a generalized vascular dysplasia which also involves the central nervous system. The neurological manifestations of the disease are due either to primary intracranial or spinal vascular lesions or to neurological complications of other visceral lesions, notably those of the lung (arteriovenous fistulae). The prevention of ischaemic or infectious cerebral accidents rests on the anatomical (excision) or functional (selective embolization) exclusion of pulmonary arteriovenous fistulae, when present.
遗传性出血性毛细血管扩张症是一种全身性血管发育异常疾病，也累及中枢神经系统。该疾病的神经学表现要么归因于原发性颅内或脊髓血管病变，要么归因于其他内脏病变（尤其是肺部病变，如动静脉瘘）的神经学并发症。当存在肺动静脉瘘时，预防缺血性或感染性脑意外取决于对其进行解剖学上的（切除）或功能性的（选择性栓塞）排除。
