Van der Merwe P L, Kalis N N, Gie R P, Dumoulin M, Gewillig M
Department of Paediatrics and Child Health, University of Stellenbosch and Tygerberg Hospital, W. Cape.
S Afr Med J. 1996 Jun;86 Suppl 3:C137-41.
Two patients with partial absence of the right and left pulmonary veins respectively are described. Congenitally absent pulmonary veins are a rare phenomenon and the diagnosis is often missed or delayed. When children present with haemoptysis and/or recurrent respiratory infections with no obvious underlying cause, absence of the pulmonary veins must be part of the differential diagnosis. Special investigations to be done in these patients are chest roentgenograph to compare the lung volumes, radio-isotope scan, echocardiography and cardiac catheterisation. Magnetic resonance imaging may be helpful in defining the cause and site of obstruction of the pulmonary veins. Depending on the cause, surgery might be considered.
本文描述了两名分别存在右肺静脉和左肺静脉部分缺如的患者。先天性肺静脉缺如是一种罕见现象，诊断常常被漏诊或延误。当儿童出现咯血和/或反复呼吸道感染且无明显潜在病因时，肺静脉缺如必须列入鉴别诊断。这些患者需进行的特殊检查包括胸部X线片以比较肺容积、放射性核素扫描、超声心动图和心导管检查。磁共振成像可能有助于明确肺静脉梗阻的原因和部位。根据病因，可考虑手术治疗。
