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大阴唇骨外间叶性软骨肉瘤

Extraskeletal mesenchymal chondrosarcoma of the labium majus.

作者信息

Lin J, Yip K M, Maffulli N, Chow L T

机构信息

Department of Clinical Oncology, Prince of Wales Hospital, Shatin, New Territories, Hong Kong.

出版信息

Gynecol Oncol. 1996 Mar;60(3):492-3. doi: 10.1006/gyno.1996.0080.

DOI:10.1006/gyno.1996.0080
PMID:8774664
Abstract

Extraskeletal mesenchymal chondrosarcoma is a rare tumor. It has been noted to occur most commonly in muscle and the central nervous system. It has never been reported to occur in the soft tissues of the anogenital region. We report the first such case, occurring in a 40-year-old woman who presented with a 1-year history of a mass originating in the left labium majus. After extensive local resection and lymph node dissection she remains disease free after 40 months follow-up.

摘要

骨外间叶性软骨肉瘤是一种罕见的肿瘤。据记载,它最常发生于肌肉和中枢神经系统。从未有过其发生于泌尿生殖区域软组织的报道。我们报告首例这样的病例,患者为一名40岁女性,有一个起源于左侧大阴唇的肿物,病史1年。经过广泛的局部切除和淋巴结清扫,在40个月的随访后她仍无疾病复发。

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Extraskeletal mesenchymal chondrosarcoma of the labium majus.大阴唇骨外间叶性软骨肉瘤
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Extraskeletal myxoid chondrosarcoma of the vulva: A case report.外阴部骨外黏液样软骨肉瘤:病例报告
Oncol Lett. 2015 Oct;10(4):2095-2099. doi: 10.3892/ol.2015.3586. Epub 2015 Aug 11.
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Extraskeletal myxoid chondrosarcoma with small bowel metastasis causing bowel obstruction.伴有小肠转移导致肠梗阻的骨外黏液样软骨肉瘤。
Case Rep Oncol Med. 2012;2012:621025. doi: 10.1155/2012/621025. Epub 2012 Nov 18.