Dorman C A
J Wound Ostomy Continence Nurs. 1996 Mar;23(2):73-9. doi: 10.1016/s1071-5754(96)90064-9.
Gardner's syndrome is a genetic disease that carries a 100% risk of malignant degeneration if left untreated. The syndrome is characterized by the presence of numerous colon polyps, along with a wide variety of extracolonic manifestations. The presence of these extracolonic manifestations increase morbidity and make treatment more difficult. The surgical procedure commonly used to manage the disease is total colectomy with creation of an ileoanal reservoir. The incidences of intestinal obstruction, genitourinary obstruction, septicemia, and fistula formation increase with the growth of desmoid tumors, which are one of the extracolonic manifestations of the disease. The ET nurse plays an essential role in the care of the patient with Gardner's syndrome. Whether acting as a consultant or primary care provider, the ET nurse provides emotional support, educates, and establishes a plan of care to manage the ostomies, skin problems, complex wounds, and fistulas associated with Gardner's syndrome.
加德纳综合征是一种遗传性疾病，如果不治疗，发生恶性变的风险为100%。该综合征的特征是存在大量结肠息肉，以及各种各样的结肠外表现。这些结肠外表现的存在会增加发病率，并使治疗更加困难。常用于治疗该疾病的外科手术是全结肠切除术并创建回肠肛管储袋。随着硬纤维瘤（该疾病的结肠外表现之一）的生长，肠梗阻、泌尿生殖系统梗阻、败血症和瘘管形成的发生率会增加。造口治疗护士在加德纳综合征患者的护理中起着至关重要的作用。无论是作为顾问还是初级护理提供者，造口治疗护士都提供情感支持、进行教育，并制定护理计划，以处理与加德纳综合征相关的造口、皮肤问题、复杂伤口和瘘管。
