Prasad V S, Reddy D R, Murty J M
Department of Neurosurgery, Nizam's Institute of Medical Sciences, Hyderabad, India.
Childs Nerv Syst. 1996 Jan;12(1):48-51. doi: 10.1007/BF00573856.
Two cases of cervico-dorsal neurenteric cysts are presented, one located dorsal and the other ventral to the spinal cord, with associated Klippel-Feil anomaly, meningocele, spinal dysraphism and possibly spinal cord malformation. One patient was operated on as a neonate for a cervico-thoracic meningocele and presented during adolescence with spastic quadriparesis. Imaging revealed spina bifida, a dorsally located neurenteric cyst and a tendency towards split cord malformation. The other child presented with cervico-thoracic kyphoscoliosis and paraparesis. Imaging demonstrated persistence of a cervico-thoracic remnant of the primitive neurenteric canal through the upper thoracic spine.
本文报告了两例颈胸段神经肠囊肿,一例位于脊髓背侧,另一例位于脊髓腹侧,同时伴有Klippel-Feil畸形、脊膜膨出、脊柱裂以及可能存在的脊髓畸形。一名患者在新生儿期因颈胸段脊膜膨出接受手术,青春期出现痉挛性四肢瘫。影像学检查显示脊柱裂、位于背侧的神经肠囊肿以及脊髓纵裂畸形倾向。另一名儿童表现为颈胸段脊柱后凸侧弯和双下肢轻瘫。影像学检查显示原始神经肠管的颈胸段残余部分持续存在于上胸椎水平。