Fernandes E T, Custer M D, Burton E M, Boulden T F, Wrenn E L, Whittle A P, Edwards O P
Department of Surgery, LeBonheur Children's Medical Center, Memphis, TN.
J Pediatr Surg. 1991 Jan;26(1):108-10. doi: 10.1016/0022-3468(91)90444-x.
Neurenteric cysts are rare, with fewer than 30 cases noted in the literature. We report the case of a newborn infant with respiratory distress caused by a large neurenteric cyst that was identified by prenatal ultrasound. Treatment consisted of excision of the mass through a right posterolateral thoracotomy. The cyst adhered to the spine at the level of the first thoracic vertebra and communicated with the jejunum through a posterior diaphragmatic defect. Postoperative studies with magnetic resonance imaging (MRI) and computed tomography (CT) disclosed an anterior meningocele and tethering of the spinal column. This is the second reported case of a neurenteric cyst demonstrated by prenatal ultrasound. The presence of an intrathoracic cyst associated with spinal abnormalities is characteristic of this anomaly. With imaging techniques such as MRI and CT, we may detect residual intraspinal disease associated with neurenteric cysts.
神经管囊肿非常罕见，文献报道的病例不足30例。我们报告了1例因大型神经管囊肿导致呼吸窘迫的新生儿病例，该囊肿在产前超声检查时被发现。治疗方法是通过右后外侧开胸手术切除肿块。囊肿在第一胸椎水平附着于脊柱，并通过膈肌后部缺损与空肠相通。术后磁共振成像（MRI）和计算机断层扫描（CT）检查显示有前侧脑脊膜膨出和脊柱拴系。这是第二例经产前超声证实的神经管囊肿病例。胸腔内囊肿伴有脊柱异常是这种畸形的特征。借助MRI和CT等成像技术，我们可以检测出与神经管囊肿相关的脊柱内残留病变。
