系统性“哑铃状”血管外皮细胞瘤。

A systemic "dumb-bell" haemangiopericytoma.

作者信息

Tancioni F, Gaetani P, Tartara F, Villani L, Martelli A, Rodriguez y Baena R

机构信息

Department of Surgery, IRCCS Policlinico S. Matteo, Italy.

出版信息

Acta Neurochir (Wien). 1996;138(7):884-5. doi: 10.1007/BF01411268.

DOI:10.1007/BF01411268

PMID:8869718

Abstract

Systemic haemangiopericytoma is a rare soft tissue tumour originating from pericytes which are contractile pericapillary cells, and represents less than one percent of all vascular neoplasms. The most common site of involvement is the thigh followed by the retroperitoneum, while the paraspinal location is very rare. We report the first case of systemic "dumb-bell" haemangiopericytoma illustrated radiologically, which mimick, a dorsal "dumb-bell" neurinoma.

摘要

系统性血管外皮细胞瘤是一种罕见的软组织肿瘤，起源于周细胞，即具有收缩能力的毛细血管周围细胞，在所有血管肿瘤中占比不到1%。最常受累的部位是大腿，其次是腹膜后，而脊柱旁部位非常罕见。我们报告了首例经放射学证实的系统性“哑铃状”血管外皮细胞瘤病例，该病例酷似背部“哑铃状”神经鞘瘤。