Baur G M, Porter J M, Bardana E J, Wesche D H, Rösch J
Ann Surg. 1977 Aug;186(2):184-9. doi: 10.1097/00000658-197708000-00010.
Ten patients presenting with a history of the acute onset of hand ischemia have undergone detailed clinical, immunologic, and arteriographic evaluation. The disease is characterized by the acute onset of hand ischemia proceeding to fingertip ulceration, in the absence of recognized systemic disease. None of the patients had any evidence of large artery obstruction. Arteriography showed diffuse obstruction of the palmar and digital arteries. No evidence was found in any patient of any systemic disease process associated with small artery obstruction. These patients are suspected of having a previously unreported variant of hypersensitivity angiitis. Patients are left with permanent obstruction of the palmar and digital arteries. Follow-up suggests the disease in non-recurrent and is characterized by progessive clinical improvement associated with the development of collateral circulation. Conservative management of the condition is recommended.
十名有手部缺血急性发作病史的患者接受了详细的临床、免疫学和动脉造影评估。该疾病的特征是在无公认的全身性疾病的情况下，手部缺血急性发作并发展至指尖溃疡。所有患者均无大动脉梗阻的证据。动脉造影显示掌部和指部动脉弥漫性梗阻。在任何患者中均未发现与小动脉梗阻相关的任何全身性疾病过程的证据。这些患者被怀疑患有先前未报道过的超敏性血管炎变体。患者的掌部和指部动脉出现永久性梗阻。随访表明该疾病不会复发，其特点是随着侧支循环的发展临床逐渐改善。建议对该病症进行保守治疗。
