[The scimitar syndrome in children. Apropos of 3 cases].

The authors describe three new cases in children of abnormal right pulmonary venous drainage into the inferior vena cava, associated with sequestration of the right lower lobe and dextrocardia caused by right pulmonary hypoplasia with a scimitar sign. The term scimitar syndrome used in the literature is to some extent inaccurate as it is neither constant nor pathognomonic. The authors have reviewed 45 paediatric cases reported in the literature and compared the different clinical, diagnostic and therapeutic aspects with their patients. To their knowledge they report the first case in childhood with right lobar sequestration, which received its blood supply from an abnormal artery arising from the right internal mammary artery.