Fujita Y, Yoshimura T, Miyamura H, Kanazawa H, Imaizumi K, Takahashi Y, Fukuda J, Aono T, Eguchi S
Kyobu Geka. 1989 Apr;42(4):334-8.
An one-year old child with Scimitar syndrome (anomalous drainage of the right pulmonary vein to inferior vena cava with right lung hypoplasia) associated with left side pulmonary hypertension and right pulmonary artery stenosis underwent surgical repair. The anomalous pulmonary vein was anastomosed to right atrium with 10 mm PTFE graft interposition and drained to left atrium through equine pericardial intra-atrial baffle. The stenotic portion of right pulmonary artery was enlarged with porcine pericardial patch. To our knowledge, this is the first successful surgical case of Scimitar syndrome with pulmonary hypertension in childhood reported in literature. A repair of anomalous pulmonary venous drainage to inferior vena cava in childhood is difficult, and a meticulous selection of surgical procedure is necessary.
一名患有弯刀综合征（右肺静脉异常引流至下腔静脉伴右肺发育不全）并伴有左侧肺动脉高压和右肺动脉狭窄的1岁儿童接受了手术修复。异常肺静脉通过10毫米聚四氟乙烯移植物吻合至右心房，并通过马心包房间隔挡板引流至左心房。右肺动脉狭窄部分用猪心包补片扩大。据我们所知，这是文献报道的首例儿童弯刀综合征合并肺动脉高压的成功手术病例。儿童期将异常肺静脉引流至下腔静脉的修复手术难度较大，因此必须精心选择手术方式。
