Delap T G, Kaberos A, Dowling P, Rees J, Golding-Wood D
E.N.T. Department, Royal Free Hospital, London, UK.
Int J Pediatr Otorhinolaryngol. 1996 Oct;37(2):179-91. doi: 10.1016/0165-5876(96)01399-7.
Fibro-osseous dysplasia is a developmental non familial, benign anomaly of bone development occurring in single or multiple bones, characterised by the replacement of normal bone by fibro-osseous tissue. We describe the case of a fourteen year old boy, which illustrates many of the difficulties confronting surgeons dealing with this uncommon condition. Complete surgical excision was required, before a definitive histological diagnosis could be established. We report the clinical, radiological and pathological features of this unusual case. We review the pathology of the condition and discuss the approaches to surgical management.
骨纤维发育异常是一种非家族性的发育性骨发育良性异常，可发生于单骨或多骨，其特征是正常骨被纤维骨组织替代。我们描述了一名14岁男孩的病例，该病例说明了外科医生在处理这种罕见病症时面临的许多困难。在做出明确的组织学诊断之前，需要进行完整的手术切除。我们报告了这一罕见病例的临床、放射学和病理学特征。我们回顾了该病症的病理学并讨论了手术治疗方法。
