Sbokos C G, McMillan I K
Br J Dis Chest. 1977 Jul;71(3):183-97. doi: 10.1016/0007-0971(77)90109-7.
Agenesis of the lung is rare. The cases of ten patients with this malformation are recorded and illustrated. Most had congenital malformation of other organs, especially the heart, as well. All had hypoplasia of the pulmonary artery or its branches. A pantaloon-like appearance of the trachea and the main bronchi on the bronchograms is described. Exercise tolerance was impaired in all patients.
肺发育不全很罕见。记录并展示了10例患有这种畸形的病例。大多数患者还伴有其他器官的先天性畸形,尤其是心脏。所有患者都有肺动脉或其分支发育不全的情况。文中描述了支气管造影显示的气管和主支气管呈马裤样外观。所有患者的运动耐量均受损。