[Associated complication of biliary atresia: cystic dilatation of intrahepatic biliary system].

Cystic dilatation of intrahepatic biliary system (CDIB) was observed on 10 postoperative patients with biliary atresia (BA). Fever, jaundice and alcoholic stool were found when CDIB was diagnosed with ultrasonography and computed tomography assertained by cholangiography. CDIB was divided into three groups by the shape of intrahepatic biliary system. They were group A (n = 3); solitary non-communicating cyst, group B (n = 1); solitary communicating cyst and group C (n = 6); multi-cystic dilatation. Treatments of CDIB were percutaneous transhepatic bile drainage (PTBD) and reanastomosis of hepatic portoenterostomy. All of our patients of group A and B were doing well after PTBD in two and re-do Kasai operation in two. However, out of 6 patients of group C, two died without any treatments, three were transplanted liver from their parents and the rest one is still in the hospital and PTBD is continued. Outcome of CDIB is good in group A and B, and poor in group C.