Sugiyama K, Hirano A, Llena J F, Goodrich J T, Uozumi T, Kurisu K, Harada K
Division of Neuropathology, Montefiore Medical Center, Albert Einstein College of Medicine.
Noshuyo Byori. 1996 Apr;13(1):57-60.
We report the case of a 16-year-old boy who presented with mesenchymal chondrosarcoma involving the ethmoid sinus, right orbit, nasal cavity, and anterior cranial fossa. The tumor was totally resected by craniofacial surgery; the patient's postoperative course was uneventful. Microscopically, the tumor was composed of highly cellular undifferentiated small cells, alternating with zones of cartilaginous tissues. Mesenchymal chondrosarcoma is a rare, aggressive variant of chondrosarcoma, which might be encountered more frequently due to the advances in neuroimaging and surgical procedures.
我们报告了一例16岁男孩，其患有间叶性软骨肉瘤，累及筛窦、右眼眶、鼻腔和前颅窝。该肿瘤通过颅面外科手术完全切除；患者术后恢复顺利。显微镜下，肿瘤由高度细胞化的未分化小细胞组成，并伴有软骨组织区域。间叶性软骨肉瘤是软骨肉瘤中一种罕见的侵袭性变体，由于神经影像学和外科手术的进展，其可能会更频繁地被发现。
