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[毛细胞白血病的不寻常病程,伴有显著的腹部淋巴结病、角膜白血病浸润和皮肤改变]

[An unusual course in hairy-cell leukemia with marked abdominal lymphadenopathy, leukemic infiltration of the cornea and skin changes].

作者信息

Zák P, Chrobák L, Podzimek K, Hejcmanová D, Voglová J, Dulícek P, Mirová S

机构信息

Oddĕlení klinické hematologie FN, Hradec Králové.

出版信息

Vnitr Lek. 1996 Jul;42(7):463-6.

PMID:8928422
Abstract

The authors describe a female patient suffering from hairy-cell leukaemia. Already at the onset of the disease, apart from marked splenomegaly, sonography revealed marked retroperitoneal lymphadenopathy. During the subsequent course skin changes developed such as vasculitis and leukaemic infiltrates of the cornea on both eyes. The patient was successfully treated with 2-chlorodeoxyadenosine (2-CdA, Leustatin).

摘要

作者描述了一名患有毛细胞白血病的女性患者。在疾病发作时,除了明显的脾肿大外,超声检查还发现明显的腹膜后淋巴结病。在随后的病程中,出现了皮肤变化,如血管炎和双眼角膜的白血病浸润。该患者用2-氯脱氧腺苷(2-CdA,氯法拉滨)成功治疗。

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