Navascues del Río J A, Luque Mialdea R, Cerdá Berrocal J, Martín Crespo R, Arrojo Vila F
Servicio de Urología Pediátrica, Hospital General Universitario Gregorio Marañón, Madrid.
Actas Urol Esp. 1996 Jun;20(6):564-8; discussion 568-9.
We have treated seven children with multicystic dysplastic kidney during the last 15 years. Three of then presented contralateral upper urinary tract anomalies. Four cases were diagnosed during prenatal period and three during the first term of life. We did analytic kidney function evaluation, ultrasound examination, voiding cystourethrography, radionuclide scan, gammagraphy, excretory urography and urinary cultures in all cases. We have found a vesicoureteral reflux with a bifid pelvis associated in the same child and two other cases with nonobstructive hydronephrosis. The child with vesicoureteral reflux presented also ipsilateral anomalies like a bladder diverticulum and an incomplete urethral duplication. One child with hydronephrosis opposite to the multicystic dysplastic kidney, also presented a bowel malrotation and a congenital cardiopathy, as extra-urologic associated anomalies.
在过去15年中，我们治疗了7例多囊性发育不良肾患儿。其中3例出现对侧上尿路异常。4例在孕期被诊断，3例在出生后第一年内被诊断。我们对所有病例都进行了肾功能分析评估、超声检查、排尿性膀胱尿道造影、放射性核素扫描、γ照相、排泄性尿路造影和尿培养。我们发现1例患儿同时存在膀胱输尿管反流和双肾盂，另外2例存在非梗阻性肾积水。患有膀胱输尿管反流的患儿还存在同侧异常，如膀胱憩室和不完全性尿道重复畸形。1例与多囊性发育不良肾相对侧患有肾积水的患儿，还存在肠旋转不良和先天性心脏病等泌尿系统外相关异常。
