Leborgne J, Lartigue S, Fiche M, Lerat F, Gibaud H, Guiberteau-Canfrère V, Bouvier S, Lehur P A
Clinique chirurgicale II, hôpital G.R. Laënnec, Nantes.
Chirurgie. 1996;121(3):163-6; discussion 167.
Cystic dystrophy in heterotopic pancreas is characterized by the presence in the duodenal thickened muscularis of cysts corresponding to dilated ducts lined with exocrine epithelium. The pancreas proper is normal. Cystic dystrophy in heterotopic pancreas occurs mostly in men, in the periampullary region. Two cases, revealed by duodenal stenosis, are reported here. Symptoms and morphologic investigations favoured a diagnosis of malignancy: in one case, partial portal thrombosis was observed; this complication has not been previously described in association with cystic dystrophy in heterotopic pancreas. Endosonography was non-contributory in these 2 cases because of duodenal stenosis. A pancreaticoduodenectomy was performed associated in one case with portal thrombectomy. Pathologic findings allowed diagnosis of cystic dystrophy in heterotopic pancreas.
异位胰腺的囊性营养不良表现为十二指肠增厚肌层内存在与由外分泌上皮衬里的扩张导管相对应的囊肿。胰腺本身正常。异位胰腺的囊性营养不良多见于男性,发生于壶腹周围区域。本文报告了2例因十二指肠狭窄而发现的病例。症状和形态学检查倾向于恶性肿瘤的诊断:1例观察到部分门静脉血栓形成;这种并发症以前未被描述为与异位胰腺的囊性营养不良相关。由于十二指肠狭窄,这2例病例的内镜超声检查没有提供有用信息。1例患者在进行胰十二指肠切除术的同时还进行了门静脉血栓切除术。病理检查结果确诊为异位胰腺的囊性营养不良。