Xue Y, Pan Y, Liu Z, Li J, Guo Y, Xie X
Jiangsu Institute of Hematology, Leukemia Research Unit, First Affiliated Hospital of Suzhou Medical College, People's Republic of China.
Cancer Genet Cytogenet. 1996 Nov;92(1):18-23. doi: 10.1016/s0165-4608(96)00112-4.
Acute myeloblastic leukemia (AML) with tetraploidy is rare. There have been only six such cases studied with banding techniques in the literature. Two were diagnosed as having AML-M2 and found to have similar near-tetraploid karyotypes with t(8;21) and missing Y chromosomes. We report two further cases of AML with tetraploid or near-tetraploid clones characterized by two t(8;21) and other chromosomal changes. Their cytogenetic findings were compatible with the diagnosis of AML-M2. Giant and bizarre blasts were seen on bone marrow (BM) smears from both cases. Immunologically, the blasts express CD2, CD15, and HLA-DR in case 1 and CD2 and CD65 in case 2. Cytogenetic studies on BM cells at diagnosis revealed that both cases had three related abnormal clones besides a normal one: 46,XY,t(8;21) (2%)/46,idem,add(7)(q31)(6.8%)/92, idem x 2 (80.6%) for case 1; and 46,XX,t(8;21)(13.4%)/47, idem,+4 (46.3%)/94,idem x 2 (39.1%) for case 2. Flow cytometric analysis displayed two cell populations in the former: one was in the diploid range and the other was in the tetraploid range. The patients did not obtain complete remissions and survived four and six months, respectively. These results indicate that tetraploid or near-tetraploid clones are secondary events which are associated with t(8;21) leukemia and may be associated with poor prognostic significance.
四倍体急性髓系白血病(AML)较为罕见。文献中仅有6例采用显带技术研究的此类病例。其中2例被诊断为AML-M2,发现具有相似的近四倍体核型,伴有t(8;21)且Y染色体缺失。我们报告另外2例AML病例,其具有四倍体或近四倍体克隆,特征为两个t(8;21)及其他染色体改变。它们的细胞遗传学结果与AML-M2的诊断相符。两例患者的骨髓涂片均可见巨大且怪异的原始细胞。免疫表型方面,病例1的原始细胞表达CD2、CD15和HLA-DR,病例2的原始细胞表达CD2和CD65。诊断时对骨髓细胞进行的细胞遗传学研究显示,两例患者除正常克隆外均有3个相关异常克隆:病例1为46,XY,t(8;21) (2%)/46,idem,add(7)(q31)(6.8%)/92, idem x 2 (80.6%);病例2为46,XX,t(8;21)(13.4%)/47, idem,+4 (46.3%)/94,idem x 2 (39.1%)。流式细胞术分析显示前者有两个细胞群:一个处于二倍体范围,另一个处于四倍体范围。这两名患者均未获得完全缓解,分别存活了4个月和6个月。这些结果表明,四倍体或近四倍体克隆是与t(8;21)白血病相关的继发事件,可能具有不良预后意义。