Ando H, Kaneko K, Ito F, Seo T, Watanabe Y, Ito T
Department of Surgery, Branch Hospital, University of Nagoya School of Medicine, Japan.
J Am Coll Surg. 1996 Dec;183(6):543-7.
The cause of extrahepatic portal vein obstruction in childhood is unknown. We investigated the anatomical features of extra hepatic portal vein obstruction to clarify its cause.
We studied portal venous anatomy in 10 patients with extrahepatic portal vein obstruction without hepatic disturbances ranging in age from 1 to 7 years (mean age, 4.2 years) using ultrasonography, portal venography, cholangio-computed tomography, and magnetic resonance imaging.
The extrahepatic portal vein was not obliterated, but it crossed over the common bile duct from the left to the right side at the cranial level of the pancreas and ran in a cranial direction along the right side of the common bile duct or coiled itself around the bile duct. Thus, the extrahepatic portal vein formed a tortuous eta-shape.
The portal vein was not obstructed in patients with extrahepatic portal vein obstruction but formed a characteristic eta-shape by coiling itself around the common bile duct, suggesting that extrahepatic portal vein obstruction has an embryological cause.
儿童肝外门静脉阻塞的病因尚不清楚。我们研究了肝外门静脉阻塞的解剖学特征以阐明其病因。
我们使用超声检查、门静脉造影、胆管计算机断层扫描和磁共振成像，对10例年龄在1至7岁（平均年龄4.2岁）无肝脏病变的肝外门静脉阻塞患者的门静脉解剖结构进行了研究。
肝外门静脉未闭塞，但在胰腺头侧水平从左侧跨越至右侧胆总管，并沿胆总管右侧向上走行或盘绕在胆管周围。因此，肝外门静脉形成了一个迂曲的η形。
肝外门静脉阻塞患者的门静脉未受阻，但通过盘绕在胆总管周围形成了特征性的η形，提示肝外门静脉阻塞有胚胎学原因。
