Amann G, Berger A, Rokitansky A
Institute of Clinical Pathology, University of Vienna, Austria.
Pathol Res Pract. 1996 Oct;192(10):1039-43; discussion 1044. doi: 10.1016/S0344-0338(96)80046-X.
A case of a congenital perineal tumor in a male infant is described, which consisted of separated fat and smooth muscle tissue in nodular arrangement. According to its clinical presentation, this lesion would be grouped into the category of so called "accessory scrotum," as part of the entity of ectopic scrotum. Based on our case and on a review of the literature, the possibility is raised that this labelling may be inappropriate on grounds of etiology and pathomorphology. It is suggested to consider similar lesions as the result of a perineal hamartomatous fat tissue overgrowth with transposed scrotal skin, which may or may not show additional hamartomatous proliferation of smooth muscle bundles, and to label them "perineal lipoma/lipoblastoma with ectopic scrotal skin" or "perineal collision-hamartoma" in the case of a prominent isolated smooth muscle component.
本文描述了一例男婴先天性会阴部肿瘤，该肿瘤由结节状排列的分离脂肪和平滑肌组织组成。根据其临床表现，此病变应归类为所谓的“副阴囊”，作为异位阴囊实体的一部分。基于我们的病例并结合文献回顾，有理由认为这种分类可能因病因和病理形态学而不合适。建议将类似病变视为会阴部错构瘤性脂肪组织过度生长并伴有阴囊皮肤移位的结果，其可能显示或不显示平滑肌束的额外错构瘤性增殖，对于突出的孤立平滑肌成分的病例，可将其标记为“伴有异位阴囊皮肤的会阴部脂肪瘤/脂肪母细胞瘤”或“会阴部碰撞性错构瘤”。
